Lymphangioma:
Often apparent in the first decade of life, this relatively uncommon
tumor consists of large serum filled spaces lined by endothelial
cells. The lesions can be located deep within the orbit
or in the eyelids. With valsalva or a upper respiratory tract
infection, lymphangiomas may increase in size and be more noticeable.
However, patients may not be aware of the lesion until there
is an abrupt onset of proptosis. This is due to hemorrhage
from capillaries into the serum filled spaces, often described
as a "chocolate cyst". In younger children, if
the lesion is large, strabismus and ambylopia can be a problem.
CT scans
can vary in presentation. This patient has a mass in the lateral
cone that is compressing the globe. Since the lesion
is vascular, not encapsulated and often infiltrates around normal
orbital structures, complete resection is usually not successful
and debulking is only performed in severe cases. Histopathologically,
the endothelial-lined spaces have no pericytes or smooth muscle
in the in their wall. There are scattered follicles of lymphoid
tissue with interstitial capillaries throughout. Back to Orbit